Erdheim-Chester disease with a late onset cardiovascular manifestations: A case report

نویسندگان

چکیده

Introduction: Erdheim-Chester disease (ECD) is an uncommon non Langerhans cell histiocytosis. Bilateral symmetric sclerosis of the long bones and probable multiorgan involvement are main manifestations this condition. Here, we report a case ECD showing diffuse thickening aorta’s entire wall pericardial effusion.

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ژورنال

عنوان ژورنال: Journal of clinical images and medical case reports

سال: 2023

ISSN: ['2766-7820']

DOI: https://doi.org/10.52768/2766-7820/2315